This case demonstrates relatively typical appearances of a bone forming osteosarcoma of the distal femur typical location in a 17yearold typical age. Rotationplasty compromise between amputation and limb salvage mc used for osteosarcoma of the distal femur in skeletally immature patients. The first radiograph demonstrates an illdefined, mixed lytic and sclerotic mass. Enchondroma is the name given to a type of a noncancerous growth or tumor which develops in the cartilage within the bones. We present nine patients with osteosarcomas of the femur treated at our institution between 2003 and 2010 with a mean followup of 27 6 to 56 months. There is an enchondroma of distal femur with typical stippled cartilage type matrix calcification. This chapter will highlight the clinical presentation, diagnosis, and treatment of osteosarcoma.
Osteosarcoma is very rare, but it is the most common type of bone cancer in children and teens. The portable document format pdf is a file format developed by adobe in the 1990s to present documents, including text formatting and images, in a manner. Osteosarcoma is a kind of bone cancer that most often affects children, teenagers, and young adults between the ages of 10 and 20. Localized chondrosarcoma has not spread out of the bone where the cancer started. A rare case of lowgrade myofibroblastic sarcoma of the. Distal femur resection with endoprosthetic reconstruction. In april 2005, after finishing up an 8th month yoga teacher training program, i saw an orthopedic doctor about a lump on my outer left thigh that had started to cause pain above my. Pathological radiological signs are often evident by the time of diagnosis. The next most common place is in the humerus, the upper arm. A read is counted each time someone views a publication summary such as the title, abstract, and list of authors, clicks on a figure, or views or downloads the fulltext. Different ways to access pdf files with firefox firefox help. An osteosarcoma os or osteogenic sarcoma ogs or simply bone cancer is a cancerous tumor in a bone.
The cancer most often grows in the ends of long bones, especially the bottom of the thigh bone femur and the top of the larger shin bone tibia. Chondrosarcoma is described as either localized or metastatic. Learn how to change how pdfs are viewed in firefox with either the builtin viewer or a third party tool. The distal femur is a far more frequently affected site compared to the diaphyseal femur. The diseases rarity and its lowgrade features make an accurate diagnosis difficult in most cases. Since his tumour doesnt affect his entire femur, they will keep his hip joint and proximal upper femur in tact. Osteosarcoma definition of osteosarcoma by medical. The duration of symptoms preceding a definitive diagnosis of osteosarcoma is quite long. I was working for a cellular company in 1993, and was in the midst of dropping off new phones to several orthopedic doctors in town, when my life abruptly changed. Osteosarcoma can metastasize spread to other parts of the body. Mel was 31 when she was diagnosed with osteosarcoma at the distal femur in 1993. Pdf large volume osteosarcomas of the femur treated with. These are examples of the gross pathology specimens of resected conventional osteosarcoma, consisting of both bony and soft tissue areas.
The incidence of pathological fracture in osteosarcoma is from 5% to 12%. The patient continues to be diseasefree at oneyear followup. In literature, hemicortical resections of lowgrade malignant bone tumors and allograft reconstruction are described. Total femur replacement surgery due to a chondrosarcoma a metastatic bone cancer. Pdf computer file format was first created in 1993 by. That is when they will take most of his femur out, send it to pathology and they see how well his tumour has responded to the chemotherapy. Sara was 28 when she was diagnosed with chondrosarcoma at the distal femur. Further investigation, with inspection of medial parts of thigh showed irregular cortical line of left femur metaphysis with some hyperechogenic expansile soft tissue mass, which is fairly vascularized. In young adults, most localized osteosarcomas occur around the knee. Mri of osteosarcoma of distal femur same patient roll over the images for more information. Download free acrobat reader dc software, the only pdf viewer that lets you read, search, print, and interact with virtually any type of pdf file.
Pdfcreator allows you to convert files to pdf, merge and rearrange pdf files, create digital signatures and more. Wide resection of a parosteal osteosarcoma usually prevents local recurrence. Clinical outcome for patients with dedifferentiated. Osteosarcoma is commonly found inside the long bones of your body, such as your arm or leg bones. The differential diagnoses of this unusual tumour include various benign entities as well as other sarcomas. We describe a new method of resection and reconstruction of parosteal osteosarcoma located in the. Osteosarcoma is a malignant primary cancer of long bones. It is a benign condition and most of the time does not cause any symptoms and rarely does it require any treatment. Leiomyosarcoma of bone is just one of the variants of spindle cell sarcoma of bone characterised by the expression of desmin and other markers indicating a significant element of smooth muscle in the tumour, without osteoid production we have investigated the management and outcome of this rare type of primary malignant bone tumour. The large or giant dog breeds are those almost exclusively predisposed to the disease and the mean age of affected animals is 8 years. It may also grow on the surface of your bones or in soft tissue, such as muscles.
Chondrosarcomas can develop in any place where there is cartilage. Nine cases 4 males, 5 females of dedifferentiated chondrosarcoma were treated in our institute. An awardwinning, radiologic teaching site for medical students and those starting out in radiology focusing on chest, gi, cardiac and musculoskeletal diseases containing hundreds of lectures, quizzes, handout notes, interactive material, most commons lists and pictorial differential diagnoses. In this case, we describe a middleaged female with a primary leiomyosarcoma of the distal femur. Us of quadriceps muscle showed unremarkable structure of muscle and quadriceps tendon. Osteosarcoma is a malignant tumor that primarily affects the long bones but can also involve other bones in the body. Osteosarcoma in the distal femur two years after an. Opening pdfs in word word office support office 365. The distal femur and adjacent tibial plateau has been resected and a total knee replacement inserted. Primary leiomyosarcoma of the bone is exceedingly rare.
Total femur replacement surgery due to a chondrosarcoma. Distal femoral resection with endoprosthetic reconstruction martin malawer overview the distal femur figure 30. Pdf statistics the universe of electronic documents. Distal femur osteotomy is done at the appropriate location as determined by the preoperative imaging studies fig 1. Most commonly progressive pain sometimes waking from sleep, swelling, and a palpable mass. Although several case reports have been published on osteosarcoma of the femur, to the best of our knowledge this report is the first one with such an unusual clinical course. Primary myofibroblastic sarcoma of the bone is a rare spindle cell tumour with, to the best of our knowledge, only eight cases reported in the available english language literature. Resection of parosteal osteosarcoma of the distal part of. Osteosarcoma is the commonest primary bone sarcoma arising with an incidence of approximately 3 per million populationyear. Please use one of the following formats to cite this article in your essay, paper or report. Treatment may consist of surgery, chemotherapy, or both. Wittig, md associate professor of orthopedic surgery chief, orthopedic oncology mount sinai medical center. Specifically, it is an aggressive malignant neoplasm that arises from primitive transformed cells of mesenchymal origin and thus a sarcoma and that exhibits osteoblastic differentiation and produces malignant osteoid.
Converting from pdf to word works best with files that are mostly textfor example, business, legal, or scientific documents. In terms of size, the lesion in the distal femur of our patient had progressed much more than the lesions in the fracture fragments figure figure5b. Dedifferentiated chondrosarcomas consist of two distinguishable components. Osteosarcoma bone cancer pediatric hematologyoncology. It usually begins in a leg bone either the femur or the tibia near the knee or in the upper arm bone the humerus near the shoulder. We describe the case of a 58yearold caucasian man who. After age 20, the risk of getting a chondrosarcoma goes up until about age 75. This is a case of a 15 year old boy who presents with worsening knee pain. Parosteal osteosarcoma is a lowgrade malignant bone tumor arising from the distal femur and tibia. July, 2002 distal femur resection with endoprosthetic reconstruction 227 border and ligaments and menisci are removed. Case discussion this case demonstrates relatively typical appearances of a bone forming osteosarcoma of the distal femur typical location in a 17yearold typical age.
The tumor location was the long bone in 7 cases femur, n5. It is a procedure where the neurovascular structures and distal aspect of the limb leg are retained, and reattached to the proximal portion after the tumor has been removed. After 10ish weeks of chemo, the treatment plan calls for a limb salvage surgery. Enchondroma distal femur what doctors want you to know.
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